Pulmonary Determinants of Cardiorespiratory Fitness in Fontan Patients

This study will examine and record the patient's medical information and medical records (patient files, computer records, etc.). Physical examination, echocardiographic, electrocardiographic, laboratory, radiological, etc. evaluations are made during the routine controls of the patients. Within the scope of this study, no attempt will be made on the patients, no additional tests will be performed, or treatment changes will not be made in the patients because they are included in this study. After these records, KPET will be performed by a specialist doctor and physiotherapist for the patients who are directed to the Faculty of Physical Therapy and Rehabilitation Cardiopulmonary Rehabilitation Unit. Pulmonary function tests and respiratory muscle strength measurements will be performed on patients who have adequate rest after CPET.

Fontan Group Inclusion Criteria:Be between 8-55 years oldHaving undergone a Fontan operationClinical stability of the patients (preserved ventricular function)No change in ongoing drug therapy that adversely affects clinical stabilityAt least 1 year after the operationFontan Group Exclusion Criteria:Neurological and/or genetic musculoskeletal diseaseHaving orthopedic and cognitive problems that prevent testingThe patient's and/or family's unwillingness to participate in the studyControl Group Inclusion Criteria:Not have cardiovascular, neurological, and/or genetic musculoskeletal diseaseNot having orthopedic and cognitive problems that prevent testingThe patient's and/or family's willingness to participate in the study